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LOR

MIM.152445 1q21

Loricrin (LOR), with involucrin (IVL) (MIM.147360), is a major component of the crosslinked cell envelope of the epidermis, otherwise known as cornified cell envelope (CE), marginal, or peripheral band.

Pathology

- germline mutations in

  • Vohwinkel syndrome and ichthyosis (MIM.604117)
  • progressive symmetric erythrokeratodermia (PSEK) (MIM.602036)

See also

- cornified envelope proteins

References

- Backendorf, C.; Hohl, D. : A common origin for cornified envelope proteins? (Letter) Nature Genet. 2: 91, 1992. PubMed ID : #1303269#