Home > E. Pathology by systems > Respiratory system > Lungs > pulmonary fibrosis
pulmonary fibrosis
Tuesday 18 November 2003
According to the topography of fibrosis
bronchiolocentric fibrosis
diffuse pulmonary fibrosis (as in NSIP)
peripheral lobular fibrosis / peripheral lobular fibrosis (as in UIP)
septal interstitial fibrosis
pulmonary peribronchovascular fibrosis
pulmonary peribronchiolar fibrosis
airway-centered interstitial fibrosis (14707865)
pulmonary fibrosis with emphysema
Diagnosis
brochiolocentric fibrosis
- consider inhalation injoury and airway inflammation
- inhalation / apsiration : fume or food
- occupational pneumonia : pneumoconiosis , popcorn lung
- systemic disease with airway inflammation (IBDs DPB)
- idiopathic diseases : fibrosis , OB , DPB
diffuse fibrosis (NSIP)
periphral lobular fibrosis
References
Razzaque MS, Taguchi T. Pulmonary fibrosis: Cellular and molecular events. Pathol Int. 2003 Mar;53(3):133-45. PMID: 12608894
Kasper M, Haroske G. Alterations in the alveolar epithelium after injury leading to pulmonary fibrosis. Histol Histopathol. 1996 Apr;11(2):463-83. PMID: 8861769
Martinet Y, Menard O, Vaillant P, Vignaud JM, Martinet N. Cytokines in human lung fibrosis. Arch Toxicol Suppl. 1996;18:127-39. PMID: 8678788